[An indolent, late-metastasizing variant of fibrosarcoma characterized by alternating fibrous and myxoid areas and a whorling growth pattern. The neoplastic cells have a spindle morphology, and lack hyperchromasia or significant nuclear atypia. Approximately 40% of cases show the focal presence of collagen rosettes. A consistent, balanced t(7;16)(q32-34;p11) translocation has been identified, associated with the presence of FUS-CREB3L2 fusion protein. Most recent evidence suggests that rare cases may express the FUS-CREB3L1 fusion protein. ( NCI )]
UMLS (NCI) C1275282